累及多器官的Rosai-Dorfman病：一例预后不良的罕见病例。
Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis.
作者信息
Sendrasoa Fandresena Arilala, Ranaivo Irina Mamisoa, Raharolahy Onivola, Andrianarison Malalaniaina, Razanakoto Naina Harinjara, Ramarozatovo Lala Soavina, Rapelanoro Rabenja Fahafahantsoa
机构信息
Department of Dermatology, Joseph Raseta Befelatanana Hospital, 101 Antananarivo, Madagascar.
出版信息
Case Rep Med. 2016;2016:3920516. doi: 10.1155/2016/3920516. Epub 2016 Oct 31.
Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.
罗萨伊-多夫曼病是一种罕见的良性组织细胞增生性疾病，通常累及淋巴结。尽管已有报道称其可累及身体其他部位，但心血管系统受累极为罕见。具体而言，罗萨伊-多夫曼病累及心脏的情况极为罕见。我们报告一例36岁女性患者，患有包括心脏在内的多器官罗萨伊-多夫曼病，预后较差。
Zotero 插件