Lee Lisa, Glastonbury Christine M, Lin Doris
Department of Otolaryngology-Head and Neck Surgery, University of Cincinnati Medical Center, Cincinnati, Ohio, USA.
Ear Nose Throat J. 2007 Oct;86(10):624-7.
Rosai-Dorfman disease is a rare, benign granulomatous disease that typically presents with massive cervical lymphadenopathy. In less than 50% of cases, other soft-tissue manifestations may also be found in the head and neck. Rosai-Dorfman disease can be difficult to diagnose because of its rarity and its ability to mimic, both clinically and radiologically, more common diseases such as lymphoma. The histopathologic diagnosis can also be difficult to make, particularly when the disease exhibits extranodal manifestations. We present a case of isolated extranodal Rosai-Dorfman disease involving the carotid sheath, without the typical massive adenopathy.
罗萨伊-多夫曼病是一种罕见的良性肉芽肿性疾病，通常表现为颈部巨大淋巴结病。不到50%的病例中，头颈部也可能出现其他软组织表现。由于罗萨伊-多夫曼病罕见，且在临床和影像学上可模仿淋巴瘤等更常见疾病，因此可能难以诊断。组织病理学诊断也可能很困难，尤其是当疾病表现为结外表现时。我们报告一例孤立性结外罗萨伊-多夫曼病，累及颈动脉鞘，无典型的巨大淋巴结病。
