Rusch V W, Shuman W P, Schmidt R, Laramore G E
Department of Surgery, University of Washington, Seattle.
Cancer. 1989 Nov 1;64(9):1928-36. doi: 10.1002/1097-0142(19891101)64:9<1928::aid-cncr2820640928>3.0.co;2-y.
The authors report the case of a 39-year-old woman with a massive malignant pulmonary hemangiopericytoma. The clinical presentation and histologic findings were typical of this rare entity, but workup and treatment were challenging because of the size and location of the tumor. Magnetic resonance imaging (MRI) proved to be critical in the preoperative evaluation because of its unique ability to delineate the precise anatomical extent of this highly vascular neoplasm. Previous treatment of this patient with exploratory thoracotomy and chemotherapy had been unsuccessful. The authors used an innovative approach to treatment which included complete surgical resection via combined median sternotomy and thoracotomy, along with intraoperative and postoperative radiotherapy. The patient is disease-free 28 months after surgery.
作者报告了一例39岁患有巨大恶性肺血管外皮细胞瘤的女性病例。临床表现和组织学检查结果是这种罕见疾病的典型特征，但由于肿瘤的大小和位置，检查和治疗颇具挑战性。磁共振成像（MRI）在术前评估中被证明至关重要，因为它具有独特能力来描绘这种高度血管化肿瘤的确切解剖范围。该患者先前接受的开胸探查和化疗均未成功。作者采用了一种创新的治疗方法，包括通过正中胸骨切开术和开胸术联合进行完全手术切除，以及术中及术后放疗。患者术后28个月无疾病复发。
