Jeong Chang-Yeong, Kim Choung-Soo
Department of Otolaryngology-Head and Neck Surgery, Daejeon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, 64 Daeheung-ro, Jung-gu Daejeon, 301-723, Republic of Korea.
Ear Nose Throat J. 2016 Dec;95(12):E12-E14.
Undifferentiated pleomorphic sarcoma, previously called malignant fibrous histiocytoma, usually arises in the extremities and retroperitoneum. Primary laryngeal undifferentiated pleomorphic sarcoma is very rare, with only 63 cases having been reported in the literature as of 2015. The disease has a poor prognosis because of problems with local recurrence and metastasis. Wide resection has been recommended as a treatment modality in previous reports. We report a case of undifferentiated pleomorphic sarcoma of the vocal fold in a 64-year-old man presenting with rapid growth. The lesion was treated with type III microlaryngeal surgery followed by radiation therapy. The patient's voice was good enough for social communication, and there was no evidence of recurrence on regular examination.
未分化多形性肉瘤，以前称为恶性纤维组织细胞瘤，通常发生于四肢和腹膜后。原发性喉未分化多形性肉瘤非常罕见，截至2015年，文献中仅报道过63例。由于存在局部复发和转移问题，该疾病预后较差。在以往的报道中，广泛切除被推荐为一种治疗方式。我们报告一例64岁男性声带未分化多形性肉瘤病例，该患者肿物生长迅速。病变经III型显微喉镜手术治疗，随后进行放射治疗。患者的声音足以进行社交交流，定期检查未发现复发迹象。
