Jones R F, Warnock T H, Nayanar V, Gupta J M
Department of Neurology, Prince of Wales Children's Hospital, Randwick, New South Wales, Australia.
Neurosurgery. 1989 Oct;25(4):554-61.
Five children with ventricular dilatation (4 boys, 1 girl) had features seen on computer tomographic scan that were consistent with suprasellar arachnoid cysts. All children were investigated with a CT ventriculogram and/or CT cisternogram, and no communication with the cyst was demonstrated. Three children were seen in the 1st year of life and the remaining 2 children were between 1 and 5 years of age. Hydrocephalus and developmental delay were the most common presenting features, followed by visual disturbance, squint, or ataxia. Direct surgical decompression was performed in all 5 patients to avoid long-term placement of a ventriculoperitoneal shunt. A temporary shunt was placed in 2 children because of high intracranial pressure. Direct partial excision of the cyst wall to allow long-term drainage into the basal cisterns or ventricular system was successful in all children. The presence of subdural collections postoperatively required temporary shunting in 2 children. After follow-up for between 10 and 22 months no clinical endocrinological sequelae have been detected, but 2 children have raised serum prolactin levels. Three children are developmentally delayed; one of these has regained some skills since surgery. Direct surgical decompression of suprasellar arachnoid cysts to avoid long-term shunt placement is the preferred method of surgical treatment for this condition.
5例脑室扩张患儿(4男1女)的计算机断层扫描表现与鞍上蛛网膜囊肿相符。所有患儿均接受了CT脑室造影和/或CT脑池造影检查,未发现囊肿有交通情况。3例患儿在1岁以内就诊,其余2例患儿年龄在1至5岁之间。脑积水和发育迟缓是最常见的临床表现,其次是视力障碍、斜视或共济失调。为避免长期放置脑室腹腔分流管,所有5例患者均接受了直接手术减压。2例患儿因颅内压高而放置了临时分流管。对所有患儿成功进行了囊肿壁部分直接切除,使囊肿长期引流至基底脑池或脑室系统。术后2例患儿出现硬膜下积液,需要临时分流。随访10至22个月后,未发现临床内分泌后遗症,但2例患儿血清催乳素水平升高。3例患儿存在发育迟缓;其中1例自手术后已恢复了一些技能。直接手术减压鞍上蛛网膜囊肿以避免长期放置分流管是这种疾病首选的手术治疗方法。