Koenig Emma, Singh Bhajan, Wood Jamie
Physiotherapy Department Sir Charles Gairdner Hospital Nedlands Australia.
Department of Pulmonary Physiology and Sleep Medicine Sir Charles Gairdner Hospital Nedlands Australia; West Australian Sleep Disorders Research Institute Nedlands Australia; Faculty of Science University of Western Australia Nedlands Australia.
Respirol Case Rep. 2016 Dec 14;5(2):e00210. doi: 10.1002/rcr2.210. eCollection 2017 Mar.
Duchenne muscular dystrophy (DMD) is an X-linked recessive myopathy associated with progressive muscle weakness and wasting, loss of ambulation, respiratory insufficiency, weak cough, repeated respiratory infections, and ultimately death from respiratory failure in early adulthood. Mechanical insufflation-exsufflation (MI-E) devices, such as the CoughAssist®, are used in individuals with neuromuscular weakness to augment cough and help clear secretions; however, there is no consensus on the optimal treatment regimen. We present the challenging case of a patient with DMD admitted to a tertiary hospital with a severe lower respiratory infection, and discuss how MI-E was used by physiotherapists to assist secretion clearance and prevent further deterioration.
杜氏肌营养不良症(DMD)是一种X连锁隐性肌病,与进行性肌肉无力和萎缩、行走能力丧失、呼吸功能不全、咳嗽无力、反复呼吸道感染以及最终在成年早期死于呼吸衰竭有关。机械通气-呼气末正压通气(MI-E)设备,如CoughAssist®,用于治疗神经肌肉无力的患者,以增强咳嗽并帮助清除分泌物;然而,关于最佳治疗方案尚无共识。我们介绍了一名患有DMD的患者入住三级医院并患有严重下呼吸道感染的具有挑战性的病例,并讨论了物理治疗师如何使用MI-E来协助清除分泌物并防止病情进一步恶化。