Tikhomirova T F, Markvarde M M, Mil'kamanovich V K
Vestn Rentgenol Radiol. 1989 May-Jun(3):32-8.
External respiratory function was investigated in 33 patients with systemic scleroderma+ using roentgenopneumopolygraphy (RPPG). Respiratory changes consisted in diffuse and regional ventilation disturbance (after emphysematous, hypoventilation or mixed type), disorders of respiratory kinetics of the diaphragm, ribs and mediastinum. External respiratory functional disturbance showed direct correlation with the patients' age, period of disease and a degree of pathological activity. The type of external respiratory functional disturbance was unchanged during observation over time. The use of exercise testing showed the presence of signs of latent ventilation insufficiency in most of the patients.
采用胸部X线呼吸功能多描记图（RPPG）对33例系统性硬化症患者的肺外呼吸功能进行了研究。呼吸变化包括弥漫性和区域性通气障碍（呈气肿型、通气不足型或混合型）、膈肌、肋骨和纵隔呼吸动力学紊乱。肺外呼吸功能障碍与患者年龄、病程及病理活动程度呈直接相关。随着时间的推移，在观察期间肺外呼吸功能障碍的类型没有变化。运动试验结果显示，大多数患者存在潜在通气不足的迹象。
