Mozaffarian Kamran, Farahani Mohammad Javad, Vosoughi Amir Reza
Bone and Joint Diseases Research Center, Department of Orthopedic Surgery, Shiraz University of Medical Sciences, Shiraz, Iran.
J Clin Orthop Trauma. 2016 Oct-Dec;7(Suppl 1):5-7. doi: 10.1016/j.jcot.2016.11.003. Epub 2016 Nov 22.
Hereditary multiple exostoses, an autosomal dominant condition, is a common benign tumor which is characterized by the development of multiple osteochondromas. Bilateral dorsal and ventral involvement of scapulae is extremely rare without any reported case in the literature. An 18-year-old girl was referred because of bilateral prominent scapulae and left-sided pain on shoulder girdle motion especially at more than 90° abduction and forward flexion. Radiograph evaluation showed multiple exostoses on ventral and dorsal surfaces of body of both scapulae; hence simple excision of the lesion was impossible. The patient was symptom-free about 18 months after partial scapulectomy of left side. Partial scapulectomy seems to be an effective treatment for the sandwiched scapula between dorsal and ventral benign tumors.
遗传性多发性骨软骨瘤是一种常染色体显性疾病，是一种常见的良性肿瘤，其特征是多发骨软骨瘤的形成。双侧肩胛背侧和腹侧受累极为罕见，文献中尚无报道病例。一名18岁女孩因双侧肩胛突出以及肩胛带活动时左侧疼痛（尤其是外展和前屈超过90°时）前来就诊。X线评估显示双侧肩胛骨体的腹侧和背侧表面有多个骨软骨瘤；因此无法对病变进行单纯切除。左侧部分肩胛骨切除术后约18个月，患者无症状。部分肩胛骨切除术似乎是治疗肩胛背侧和腹侧良性肿瘤夹在中间的肩胛骨的有效方法。
