Benichou M, Balmes P, Marty-Double C H, Allieu Y
Service de Chirurgie Orthopédique et Chirurgie de la Main, Hôpital Lapeyronie CHU, Montpellier.
Ann Chir Main. 1989;8(2):150-3. doi: 10.1016/s0753-9053(89)80008-0.
The juvenile aponeurotic fibroma, isolated in 1953 by Louisa Keasbey is a rare tumour which is characterized by its recurrence and infiltration, but which has no tendency to metastasis. The case we report differs in its long-term outcome. The tumour diagnosed in a seven-year-old child has recurred locally for seven years, necessitated hand amputation, and finally developed a fibroblastic process extending to lung and pleura which caused the child's death. After this new finding in Keasbey's disease, we are led to reconsider the nosological situation in juvenile fibromatoses and its character of benign disease.
青少年腱膜纤维瘤由路易莎·基斯贝于1953年首次发现，是一种罕见肿瘤，其特点是易复发和浸润，但无转移倾向。我们报告的这例病例在长期预后方面有所不同。该肿瘤在一名7岁儿童中被诊断出，已局部复发7年，导致手部截肢，最终发展为成纤维细胞病变并蔓延至肺部和胸膜，导致患儿死亡。在基斯贝病出现这一新发现后，我们不得不重新审视青少年纤维瘤病的疾病分类情况及其良性疾病的特征。
