Ralls Matthew W, Coran Arnold G, Teitelbaum Daniel H
Department of Surgery, Section of Pediatric Surgery, University of Michigan, 1540 East Hospital Drive, Ann Arbor, Michigan, 48109-4211, USA.
Pediatr Surg Int. 2017 Apr;33(4):455-460. doi: 10.1007/s00383-016-4045-4. Epub 2016 Dec 31.
Pullthrough procedures for Hirschsprung diseases typically have favorable results. However, some children experience long-term postoperative complications comprising stooling disorders, such as intermittent enterocolitis, severe stool retention, intestinal obstruction, as well as incontinence. Reoperative Hirschsprung Disease surgery is complex. This begins with the workup after the initial presentation following primary pullthrough, continues with the definitive surgical correction with redo pullthrough, and ends with long-term follow-up of individuals. The decision tree can be varied with each patient. The operating pediatric surgeon must be able to utilize different operations and treatment options available. While lesser procedures may provide relief in a select population, those with residual aganglionosis or transition zone pathology or mechanical problems will likely require a redo pullthrough. Thus, the diagnostic workup, treatment plan, and definitive surgical care should be coordinated, and executed by an experienced, specialized team at a pediatric referral center.
先天性巨结肠症的拖出手术通常效果良好。然而,一些儿童会出现长期术后并发症,包括排便障碍,如间歇性小肠结肠炎、严重大便潴留、肠梗阻以及大便失禁。先天性巨结肠症再次手术很复杂。这始于初次拖出手术后首次就诊时的检查,接着是通过再次拖出进行确定性手术矫正,最后是对个体的长期随访。决策树可能因每个患者而异。实施手术的小儿外科医生必须能够运用现有的不同手术和治疗方案。虽然较小的手术可能会使特定人群得到缓解,但那些有残留无神经节症或过渡区病变或机械问题的患者可能需要再次拖出。因此,诊断检查、治疗计划和确定性手术护理应由儿科转诊中心经验丰富的专业团队进行协调和实施。