Arellano Lorca Javier, Yáñez Silva Ignacio, Soto Vilches Felipe, Luna Heine Andrea, Corredoira Salum Yamile
Servicio de Dermatología, Hospital Clínico San Borja Arriarán, Santiago, Chile.
Universidad Católica del Maule, Chile.
Rev Med Chil. 2016 Sep;144(9):1214-1217. doi: 10.4067/S0034-98872016000900017.
Pityriasis lichenoides et varioliformis acuta (PLEVA), pityriasis lichenoides chronica (PLC) and febrile ulceronecrotic Mucha-Habermann disease (FUMHD) are considered different manifestations of the same disease. Febrile ulceronecrotic Mucha-Habermann disease is a rare, and potentially lethal illness which is characterized by fast progression of numerous papules that converge, ulcerate and form a plaque with a necrotic center, together with hemorrhagic vesicles and pustules that are associated with high fever and variable systemic symptoms. We report a 16 years old male presenting with erythematous papules with crusts and fever. The diagnosis of febrile ulceronecrotic Mucha-Habermann disease was confirmed with the pathological study of the lesions. He was successfully treated with minocycline after a failed attempt of treatment with prednisone.
急性痘疮样苔藓样糠疹（PLEVA）、慢性苔藓样糠疹（PLC）和发热性溃疡性坏死性穆查-哈伯曼病（FUMHD）被认为是同一种疾病的不同表现形式。发热性溃疡性坏死性穆查-哈伯曼病是一种罕见且可能致命的疾病，其特征是大量丘疹迅速进展，融合、溃疡并形成具有坏死中心的斑块，同时伴有与高热和各种全身症状相关的出血性水疱和脓疱。我们报告一名16岁男性，表现为伴有结痂的红斑丘疹和发热。通过对病变进行病理研究确诊为发热性溃疡性坏死性穆查-哈伯曼病。在用泼尼松治疗失败后，他用米诺环素成功治愈。
