Scognamiglio R, Fasoli G, Nava A, Miraglia G, Valentina D, Thiene G, Dalla Volta S
Department of Cardiology, Medical School, University of Padua, Italy.
Eur Heart J. 1989 Sep;10 Suppl D:27-8. doi: 10.1093/eurheartj/10.suppl_d.27.
Right ventricular dysplasia (RVD) is an important cause of arrhythmic sudden death in young people. Echocardiographic criteria suggestive of RVD were: dilation of RV, localized bulge and dyskinesia of the inferobasal wall, structural changes of the moderator band, isolated enlargement of RV outflow tract, apical dyskinesia and trabecular disarrangement. Among 136 subjects 'at risk of high incidence of RVD', 40 had a suggestive echocardiogram. 90% of these showed lipomatous transformation at biopsy and/or developed serious ventricular arrhythmias during a mean follow-up of 42 months. Thus, echocardiography is a potent method in detecting myocardial pathology due to RVD.
右心室发育不良（RVD）是年轻人心律失常性猝死的重要原因。提示RVD的超声心动图标准为：右心室扩张、下基底部壁局部膨出和运动障碍、节制索结构改变、右心室流出道孤立性扩大、心尖运动障碍和小梁排列紊乱。在136名“RVD高发风险”受试者中，40人超声心动图有提示表现。其中90%在活检时显示脂肪化生和/或在平均42个月的随访期间发生严重室性心律失常。因此，超声心动图是检测RVD所致心肌病变的有效方法。
