墨西哥患者的无硬皮病系统性硬化症。病例报告。
Systemic Sclerosis Sine Scleroderma in Mexican Patients. Case Reports.
作者信息
Vera-Lastra Olga, Sauceda-Casas Christian Alexis, Domínguez María Del Pilar Cruz, Alvarez Sergio Alberto Mendoza, Sepulceda-Delgado Jesús
机构信息
Departamento de Medicina Interna, Unidad Médica de Alta Especialidad, Hospital de Especialidades Dr. Antonio Fraga Mouret, Centro Médico Nacional, La Raza, Instituto Mexicano del Seguro Social, México D.F., México; División de Estudios de posgrado, Facultad de Medicina, Universidad Nacional Autónoma de México, México D.F., México.
Universidad Autónoma de Sinaloa, México; Academia Mexicana de la Ciencia, México.
出版信息
Reumatol Clin (Engl Ed). 2018 Jul-Aug;14(4):230-232. doi: 10.1016/j.reuma.2016.11.004. Epub 2017 Jan 3.
UNLABELLED
Systemic sclerosis sine scleroderma (ssSSc) is a form of systemic sclerosis that is characterized by Raynaud's phenomenon (RP), visceral involvement without thickening of skin and anticentromere antibodies (ACA). We studied 10 ssSsc patients with a prevalence of 2%. The clinical signs were: RP 9/10, esophageal manifestations 8/10, pulmonary arterial hypertension 4/10, interstitial lung disease 4/10, cardiac signs 3/10 and ACA 8/10.
CONCLUSION
In patients with RP, esophageal dysmotility, interstitial lung disease and pulmonary arterial hypertension should be tested for ACA in order to establish a prompt diagnosis and treatment of ssSSc.
未标注
无硬皮病的系统性硬化症（ssSSc）是系统性硬化症的一种形式，其特征为雷诺现象（RP）、无皮肤增厚的内脏受累以及抗着丝点抗体（ACA）。我们研究了10例ssSSc患者，患病率为2%。临床体征为：RP 9/10、食管表现8/10、肺动脉高压4/10、间质性肺疾病4/10、心脏体征3/10以及ACA 8/10。
结论
对于患有RP、食管动力障碍、间质性肺疾病和肺动脉高压的患者，应检测ACA，以便及时诊断和治疗ssSSc。
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