Lopez M P J, Encila V I, Alamo S G, Monroy H J, Roxas M F T
Division of Colorectal Surgery, Philippine General HospitalUniversity of the Philippines, Taft Avenue, 1000, Manila, Philippines.
Tech Coloproctol. 2017 Feb;21(2):111-118. doi: 10.1007/s10151-016-1577-5. Epub 2017 Jan 9.
Anorectal malformations (ARMs) are rarely seen in adults, since majority of cases are corrected in infancy or childhood. The aim of this study was to describe the profile of patients who underwent definitive surgery to correct their ARM in adulthood, and to discuss the outcomes of surgery (morbidity, mortality, and function).
This retrospective study included patients 18 years old and above, managed surgically by the Division of Colorectal Surgery at the Philippine General Hospital, University of the Philippines, Manila, from January 1, 2004, to December 31, 2012. Data from the Integrated Surgical Information System and the patients' hospital records were used to fill out a Data Collection Form. Frequencies and percentages were then computed.
Eight patients were included in the study. The most common reason for consult was recurrent urinary tract infection (UTI, 25%). One patient had an imperforate anus (IA) without a fistula, and 1 patient had IA with rectal atresia, and the 6 had an IA with a fistula. All but one (87.5%) of the patients had undergone a prior diversion in infancy or childhood. Definitive surgical procedures included posterior sagittal anorectoplasty (PSARP) in 3 patients, anal transposition in 2 patients, laparotomy with colocutaneous anastomosis in two patients, and laparotomy and PSARP in 1 patient. There were 3 cases (37.5%) of postoperative complications. These complications included ureteral injury, enterocutaneous fistula, anal stricture, rectal stricture, rectovesical fistula, and recurrent rectourethral fistula. There was no reported mortality. Five patients already had their stomas reversed at the time of this writing.
Our results showed that the rarity of the disease, limited surgical experience, and a technically challenging anatomy make the management of ARMs that persist into adulthood a formidable undertaking.
肛门直肠畸形(ARMs)在成人中很少见,因为大多数病例在婴儿期或儿童期就得到了矫正。本研究的目的是描述成年后接受确定性手术矫正其ARM的患者情况,并讨论手术结果(发病率、死亡率和功能)。
这项回顾性研究纳入了2004年1月1日至2012年12月31日在菲律宾大学马尼拉市菲律宾总医院结直肠外科接受手术治疗的18岁及以上患者。来自综合手术信息系统和患者医院记录的数据用于填写数据收集表。然后计算频率和百分比。
8名患者纳入研究。最常见的就诊原因是复发性尿路感染(UTI,25%)。1例患者为无瘘的肛门闭锁(IA),1例患者为伴有直肠闭锁的IA,6例患者为伴有瘘的IA。除1例(87.5%)外,所有患者在婴儿期或儿童期都曾接受过造口术。确定性手术包括3例患者接受后矢状位肛门直肠成形术(PSARP),2例患者接受肛门移位术,2例患者接受剖腹术并结肠皮肤吻合术,1例患者接受剖腹术和PSARP。有3例(37.5%)术后并发症。这些并发症包括输尿管损伤、肠皮肤瘘、肛门狭窄、直肠狭窄、直肠膀胱瘘和复发性直肠尿道瘘。无死亡报告。在撰写本文时,5例患者的造口已回纳。
我们的结果表明,该疾病的罕见性、有限的手术经验以及具有技术挑战性的解剖结构使得对持续到成年期的ARMs进行管理成为一项艰巨的任务。