成骨不全症视网膜脱离的手术治疗：病例报告及文献综述
SURGICAL MANAGEMENT OF RETINAL DETACHMENT IN OSTEOGENESIS IMPERFECTA: CASE REPORT AND REVIEW OF THE LITERATURE.
作者信息
Fleissig Efrat, Barak Adiel
机构信息
Department of Ophthalmology, Tel Aviv Sourasky Medical Center, Sackler Faculty of Medicine, Tel-Aviv University, Tel Aviv, Israel.
出版信息
Retin Cases Brief Rep. 2019;13(1):43-46. doi: 10.1097/ICB.0000000000000527.
PURPOSE
To describe a case of scleral buckling in a patient with severe (Type III) osteogenesis imperfecta.
METHODS
Single interventional case report of a 37-year-old woman, with clinically diagnosed osteogenesis imperfecta Type III, presenting with an inferior retinal detachment of the right eye. The patient was promptly treated with scleral buckling.
RESULTS
Long-term follow-up has shown a good clinical outcome, with no recurrence of the retinal detachment. Eighteen months postsurgery, an ischemic branch retinal vein obstruction has developed in the right eye, complicated by macular edema. The patient was treated successfully with bevacizumab injections, with restoration of visual acuity to 20/25.
CONCLUSION
Scleral buckle may provide a good surgical option in selected patients with osteogenesis imperfecta, yielding excellent anatomical and functional results.
目的
描述一例患有严重（III型）成骨不全症患者的巩膜扣带术病例。
方法
对一名37岁临床诊断为III型成骨不全症的女性患者进行单例介入病例报告，该患者右眼出现视网膜下脱离。患者立即接受了巩膜扣带术治疗。
结果
长期随访显示临床效果良好，视网膜脱离未复发。术后18个月，右眼发生缺血性视网膜分支静脉阻塞，并伴有黄斑水肿。患者通过贝伐单抗注射治疗成功，视力恢复至20/25。
结论
巩膜扣带术可能为部分成骨不全症患者提供良好的手术选择，可取得优异的解剖和功能效果。
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