肺泡蛋白沉积症合并继发性噬血细胞性淋巴组织细胞增生症

Pulmonary Alveolar Proteinosis in Association with Secondary Hemophagocytic Lymphohistiocytosis.

作者信息

Lin Jenny, De Aliva, Figueiredo Lisa, Maxwell Rochelle, Wasserman Emily, Adams Kelly, Weingarten Jacqueline, Peek Giles, Miksa Michael

机构信息

Division of Pediatric Respiratory and Sleep Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.

出版信息

J Pediatr. 2017 Apr;183:191-195. doi: 10.1016/j.jpeds.2016.12.037. Epub 2017 Jan 12.

DOI:10.1016/j.jpeds.2016.12.037

PMID:28088396

Abstract

Pulmonary alveolar proteinosis (PAP) is a rare diffuse lung disease in the pediatric population. There are currently few cases documenting hemophagocytic lymphohistiocytosis as a cause for secondary PAP. We describe an ex-preterm child with secondary hemophagocytic lymphohistiocytosis, complicated by PAP and hypoxemic respiratory failure.

摘要

肺泡蛋白沉积症（PAP）是儿科人群中一种罕见的弥漫性肺部疾病。目前记录噬血细胞性淋巴组织细胞增生症作为继发性PAP病因的病例很少。我们描述了一名患有继发性噬血细胞性淋巴组织细胞增生症的早产患儿，并发PAP和低氧性呼吸衰竭。