Lambdin Jacob Trygve, Mackenzie Catherine
George Washington University School of Medicine and Health Sciences, Arlington, Virginia, USA.
George Washington University School of Medicine and Health Sciences, Stouffville, Ontario, Canada.
BMJ Case Rep. 2017 Jan 27;2017:bcr2016217290. doi: 10.1136/bcr-2016-217290.
Rumpel-Leede phenomenon (RLP), also known as acute capillary rupture syndrome (ACRS), is a rare occurrence where distal dermal capillaries rupture in response to a proximal compressive force, such as a blood pressure cuff or tourniquet. This phenomenon has been reported to occur in states of vascular fragility such as long-term steroid use, hypertension or diabetes mellitus. Here, we provide a report of RLP occurring secondary to tourniquet application in a 26-year-old woman with adult-onset Still's disease (AOSD) and a recent drug rash. In this case, the cause of the phenomenon is most likely multifactorial. Likely contributing factors include long-term steroid use for the treatment of AOSD, and increased vascular permeability secondary to the drug rash. Patients and clinicians should be aware that the treatment of AOSD may induce a state of capillary fragility and they should work together to minimise the risk of complications.
鲁姆佩尔-利德现象(RLP),也称为急性毛细血管破裂综合征(ACRS),是一种罕见情况,即远端真皮毛细血管因近端压迫力(如血压袖带或止血带)而破裂。据报道,这种现象发生在血管脆弱的状态下,如长期使用类固醇、高血压或糖尿病。在此,我们报告一例26岁成年斯蒂尔病(AOSD)并近期出现药物疹的女性因使用止血带继发鲁姆佩尔-利德现象。在该病例中,该现象的原因很可能是多因素的。可能的促成因素包括用于治疗AOSD的长期类固醇使用,以及药物疹继发的血管通透性增加。患者和临床医生应意识到AOSD的治疗可能会诱发毛细血管脆弱状态,他们应共同努力将并发症风险降至最低。