Abate Ejigayehu G, Clarke Bart L
Division of Endocrinology and Metabolism, Mayo Clinic , Jacksonville, FL , USA.
Division of Endocrinology, Diabetes, Metabolism, and Nutrition, Mayo Clinic , Rochester, MN , USA.
Front Endocrinol (Lausanne). 2017 Jan 16;7:172. doi: 10.3389/fendo.2016.00172. eCollection 2016.
Hypoparathyroidism is a rare endocrine disorder in which parathyroid hormone (PTH) production is abnormally low or absent, resulting in low serum calcium and increased serum phosphorus. The most common cause of hypoparathyroidism is parathyroid gland injury or inadvertent removal during thyroid surgery. Current treatments include supplementation with calcium and active vitamin D, with goal albumin-corrected serum calcium level in the low-normal range of 8-9 mg/dl. Complications of the disease include renal dysfunction, nephrocalcinosis, kidney stones, extracellular calcifications of the basal ganglia, and posterior subcapsular cataracts, as well as low bone turnover and increased bone density. Until January 2015, hypoparathyroidism was the only classic endocrine disease without an available hormone replacement. Recombinant human PTH 1-84, full-length PTH, is now available for a selected group of patients with the disease who are not well controlled on the current standard therapy of calcium and active vitamin D. In addition, the role of PTH replacement on quality of life, intracerebral calcifications, cataracts, improving bone turnover, and reduction of renal complications of the disease remains to be further investigated.
甲状旁腺功能减退症是一种罕见的内分泌疾病,甲状旁腺激素(PTH)分泌异常减少或缺乏,导致血清钙水平降低和血清磷水平升高。甲状旁腺功能减退症最常见的病因是甲状旁腺损伤或甲状腺手术中意外切除。目前的治疗方法包括补充钙和活性维生素D,目标是使白蛋白校正后的血清钙水平处于8 - 9mg/dl的低正常范围。该疾病的并发症包括肾功能不全、肾钙质沉着症、肾结石、基底节细胞外钙化、后囊下白内障,以及低骨转换和骨密度增加。直到2015年1月,甲状旁腺功能减退症是唯一一种没有可用激素替代疗法的经典内分泌疾病。重组人PTH 1 - 84(全长PTH)现在可用于一部分对目前钙和活性维生素D标准治疗反应不佳的该疾病患者。此外,PTH替代疗法对生活质量、脑内钙化、白内障、改善骨转换以及减少该疾病的肾脏并发症的作用仍有待进一步研究。