Nikiforov B M, Ul'rikh E V
Zh Vopr Neirokhir Im N N Burdenko. 1989 Jul-Aug(4):23-6.
The authors had under observation 21 patients with diastematomyelia--a rare congenital disease marked by the formation of a bony spicule in the vertebral canal, which splits the spinal cord and its meninges. The disease may be manifested by localized (at the level of the bony spicule) skin lesions on the back (hypertrichosis), developmental anomalies of the locomotor apparatus, and disorders of spinal cord function of various degree. The diagnosis is established on the basis of radiological examination (plain and contrast spondylographs). During surgical intervention (laminectomy) the bony spicule is removed, the dura mater surrounding it is cut, and a common sheath is formed from the dura mater for the locally split spinal cord.
作者观察了21例脊髓纵裂患者,这是一种罕见的先天性疾病,其特征是在椎管内形成骨棘,将脊髓及其脑膜分开。该疾病可能表现为背部局部(骨棘水平处)皮肤病变(多毛症)、运动器官发育异常以及不同程度的脊髓功能障碍。诊断基于放射学检查(普通和造影脊椎X线片)。在手术干预(椎板切除术)过程中,切除骨棘,切开其周围的硬脑膜,并由硬脑膜为局部裂开的脊髓形成一个共同的鞘。