Acharya Prakash, Ang Jonathan Ross, Gitler Bernard
Montefiore New Rochelle Hospital, New Rochelle, NY, USA.
University of Missouri Health Care, Columbia, MO, USA.
J Investig Med High Impact Case Rep. 2017 Jan 1;5(1):2324709616688710. doi: 10.1177/2324709616688710. eCollection 2017 Jan-Mar.
Ebstein anomaly is a rare congenital disorder that involves the tricuspid valve and the right ventricle. It is associated with interatrial communication, which allows for paradoxical embolization causing unilateral blindness. Abnormal conduction through the atrialized right ventricle leads to QRS fragmentation on electrocardiogram. Its presence suggests a more severe abnormality and a higher risk of arrhythmia. The QRS fragmentation disappears after corrective surgery with resection of the atrialized right ventricle.
埃布斯坦畸形是一种罕见的先天性疾病,累及三尖瓣和右心室。它与心房间交通有关,可导致反常栓塞,引起单眼失明。通过房化右心室的异常传导导致心电图上QRS波群碎裂。其出现提示存在更严重的异常以及更高的心律失常风险。在切除房化右心室的矫正手术后,QRS波群碎裂消失。