Rybus-Kalinowska Barbara, Kalinowski Mariusz, Teodorowicz-Rachuba Bogna, Trzaska-Sobczak Marzena, Jochem Jerzy
Katedra i Zakład Podstawowych Nauk Medycznych, Wydział Zdrowia Publicznego w Bytomiu, Śląski Uniwersytet Medyczny w Katowicach, Polska, Chorzowskie Centrum Pediatrii i Onkologii, Chorzów, Polska.
Katedra I Oddział Kliniczny Kariochirurgii, Transplantologii, Chirurgii Naczyniowej I Endowaskularnej, Wydział Lekarski w Zabrzu, Śląski Uniwersytet Medyczny w Katowicach, Polska.
Wiad Lek. 2016;69(6):829-831.
Langerhans cell histocytosis is a rare disease. LCH is reported mainly in children aged less than 15 years, however it may appear at any age. In this work, the case of 17-month boy is reported. The boy was admitted to the pediatric ophthalmology department in order to diagnose the swelling and bruising in the lower part of left orbit, which had lasted for one month before. The clinical status, various imaging techniques' results (MRI, TK and PET) and immunohistochemistry led to the final diagnosis of multisystem LCH (spread to masticator muscle and zygomatic bone). After the pharmacological therapy the total remission was achieved. Since four years the child is regularly controlled by oncologists and hematologists with no relapse reported.
朗格汉斯细胞组织细胞增多症是一种罕见疾病。朗格汉斯细胞组织细胞增多症主要报道于15岁以下儿童，但也可能出现在任何年龄。在这项工作中，报道了一名17个月大男孩的病例。该男孩因诊断左眼眶下部持续了一个月的肿胀和瘀伤而入住小儿眼科。临床状况、各种成像技术（MRI、TK和PET）的结果以及免疫组织化学检查最终确诊为多系统朗格汉斯细胞组织细胞增多症（扩散至咀嚼肌和颧骨）。经过药物治疗后实现了完全缓解。四年来，该儿童一直由肿瘤学家和血液学家定期进行检查，未报告复发情况。
