Rege Shrikant V, Tadghare Jitendra, Patil Harshad, Narayan Sharadendu
Department of Neurosurgery, Sri Aurobindo Medical College and PG Institute, Indore, Madhya Pradesh, India.
J Pediatr Neurosci. 2016 Oct-Dec;11(4):351-354. doi: 10.4103/1817-1745.199460.
Primitive neuroectodermal tumors (PNETs) are aggressive childhood malignancies and are difficult to treat. Primary intraspinal PNETs are rare. These patients have poor prognosis with short survival time even after surgery and chemoradiation. As there are no standard guidelines exist for the management of these tumors, a multidisciplinary approach has been employed with varying success. According to the review of literature, only few cases of primary intraspinal extradural PNETs have been reported. Herein, author has described a case of intraspinal, extradural PNET.
原始神经外胚层肿瘤(PNETs)是侵袭性儿童恶性肿瘤,难以治疗。原发性脊柱内PNETs很罕见。这些患者预后较差,即使经过手术和放化疗,生存时间也很短。由于目前尚无针对这些肿瘤治疗的标准指南,因此采用了多学科方法,但效果各异。根据文献综述,仅报道了少数原发性脊柱内硬膜外PNETs病例。在此,作者描述了一例脊柱内硬膜外PNETs病例。