Koretz M J, Wang S, Klein F A, Lawrence W
Division of Surgical Oncology, Medical College of Virginia, Virginia Commonwealth University, Richmond, Virginia.
Cancer. 1987 Nov 15;60(10):2484-8. doi: 10.1002/1097-0142(19871115)60:10<2484::aid-cncr2820601023>3.0.co;2-t.
Extrarenal Wilms' tumor is a very rare disease, occurring mostly in children. Sixteen cases have been reported in the world medical literature. A case of retroperitoneal extrarenal Wilms' tumor is reported in a 36-year old white male and the literature reviewed. Pathologic examination revealed both undifferentiated renal blastoma plus differentiated areas containing immature tubules and glomeruli. No evidence of extrarenal teratomatous tissue was seen. Theories for the histogenesis of this rare tumor are discussed.
肾外威尔姆斯瘤是一种非常罕见的疾病，主要发生于儿童。世界医学文献中已报道了16例。本文报告了一名36岁白人男性的腹膜后肾外威尔姆斯瘤病例，并对相关文献进行了综述。病理检查显示既有未分化的肾母细胞瘤，又有包含不成熟肾小管和肾小球的分化区域。未见肾外畸胎瘤组织证据。本文讨论了这种罕见肿瘤的组织发生学理论。
