Piatti Gioia, De Santi Maria Margherita, Torretta Sara, Pignataro Lorenzo, Soi Daniela, Ambrosetti Umberto
1 Department of Pathophysiology and Transplantation, University of Milan, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Division of Bronchopneumology, Milan, Italy.
2 Department of Human Pathology and Oncology, University of Siena, Siena, Toscana, Italy.
Ann Otol Rhinol Laryngol. 2017 Apr;126(4):322-327. doi: 10.1177/0003489417691299. Epub 2017 Feb 12.
To investigate the prevalence of otological complications derived from primary ciliary dyskinesia (PCD) in adulthood.
Twenty-three patients with diagnosed PCD underwent medical history aimed at recording the presence of ear, nose, and throat manifestations (ENT) and any surgical treatments. The ENT objectivity was annotated, and then patients were subjected to audiometric test, tympanometry, registration of otoacoustic emission, and vestibular evaluation.
Otitis media with chronic middle ear effusion (OME) during childhood was reported in 52% of the subjects, no patient had undergone ear surgery, and only 2 patients had an episode of otitis in the last year. Eleven of 23 patients showed normal hearing, 11 had a conductive hearing impairment, and 1 showed a severe sensorineural hearing loss unrelated to the syndrome. The bilateral stapedial reflex was only found in all cases of normoacusia and type A tympanogram, distortion product otoacoustic emissions (DPOAE) were present in 8 patients, and no patient had vestibular alterations.
Our study confirms a very frequent prevalence of OME in PCD during childhood. Careful monitoring of otological complications of the syndrome is always desirable, also given the high presence in adults of other manifestations in the upper airways, such as chronic rhinosinusitis and nasal polyposis.
调查成年期原发性纤毛运动障碍(PCD)所致耳科并发症的患病率。
对23例确诊为PCD的患者进行病史采集,旨在记录耳、鼻、喉表现(ENT)及任何外科治疗情况。记录ENT客观检查结果,然后对患者进行听力测试、鼓室图检查、耳声发射记录及前庭评估。
52%的受试者报告童年期有慢性中耳积液(OME)伴中耳炎,无患者接受过耳部手术,且去年仅有2例患者有中耳炎发作。23例患者中11例听力正常,11例有传导性听力障碍,1例有与该综合征无关的重度感音神经性听力损失。双侧镫骨肌反射仅在所有听力正常和A型鼓室图的病例中发现,8例患者有畸变产物耳声发射(DPOAE),无患者有前庭改变。
我们的研究证实PCD患者童年期OME的患病率非常高。鉴于该综合征患者成年期上呼吸道其他表现(如慢性鼻窦炎和鼻息肉)的高发生率,对该综合征的耳科并发症进行仔细监测始终是必要的。