Harada Kenji, Mori Kazuhiro, Ichimiya Chiyo, Terada Naho, Iima Tsutomu, Harada Takafumi, Fujisawa Kazutoshi, Kawata Atsushi, Okada Ayumi, Yamamoto Hirofumi, Fujinaga Hiroyuki
Department of Cardiovascular Medicine, Tokushima Prefectural Central Hospital, Tokushima, Japan.
Department of Pediatrics, Tokushima Prefectural Central Hospital, Tokushima, Japan.
Echocardiography. 2017 May;34(5):791-793. doi: 10.1111/echo.13497. Epub 2017 Mar 14.
Double-chambered left ventricle (DCLV) is a particularly rare congenital entity characterized by the presence of two ventricular cavities separated by an abnormal muscle band. An asymptomatic 15-year-old boy was referred to our hospital because of electrocardiographic (ECG) abnormalities. His initial transthoracic echocardiography (TTE) demonstrated a DCLV with mild left ventricular systolic dysfunction. During a 5-year follow-up period, he remained symptom free with no changes in ECG and conventional TTE findings. However, two-dimensional speckle tracking echocardiography revealed a subtle progressive deterioration of left ventricular systolic function during the 5-year follow-up.
双腔左心室（DCLV）是一种极为罕见的先天性疾病，其特征为存在两个由异常肌束分隔的心室腔。一名无症状的15岁男孩因心电图（ECG）异常被转诊至我院。他最初的经胸超声心动图（TTE）显示为双腔左心室伴轻度左心室收缩功能障碍。在5年的随访期内，他一直无症状，心电图和传统TTE检查结果无变化。然而，二维斑点追踪超声心动图显示在5年随访期间左心室收缩功能有轻微的进行性恶化。
