Chen Ping, Wang Ying-Peng, Mou Dan-Lei, Li Zheng-Yi, Qu Qiu-Min, Wang Hong-Yan, Deng Yuan, Li Xiao-Feng, Wang Ting, Xu Xian-Hao, Zhao Gang
Department of Neurology, Xijing Hospital, Fourth Military Medical University, No. 169, Changle West Road, Xi'an, 710032, China.
Department of Neurology, Beijing Aerospace General Hospital, Beijing, 100076, China.
Pathol Oncol Res. 2018 Jan;24(1):67-74. doi: 10.1007/s12253-017-0213-7. Epub 2017 Mar 15.
Thymectomy is routinely carried out in patients with myasthenia gravis (MG) and thymomas. However, there is still a dispute as to whether MG patients with thymic hyperplasia should undergo thymectomy. We aimed to investigate the pathological findings in the thymus in patients with co-existing MG and thymic hyperplasia or thymomas treated with thymectomy, as well as effects of immunosuppression. Thirty-three patients with MG were selected and grouped accordingly: patients with no thymic abnormalities, patients with thymic hyperplasia, and patients with thymomas. All patients were treated with methylprednisolone alongside immunosuppression. A separate cohort of 24 MG patients with thymic hyperplasia or thymomas and treated with thymectomy were selected. As controls, 5 patients with thymomas or thymic carcinoma without MG were selected. Expression of CD5, extracellular regulated protein kinases1/2 mitogen activated protein kinase (ERK1/2MAPKs) and CD95 ligand (FasL) in the thymus was examined. Methylprednisolone and immunosuppressive therapy are highly effective in MG patients with normal thymus tissue and MG patients with thymic hyperplasia compared to MG patients with thymomas alone. CD5 expression was highest in MG patients with thymic hyperplasia, correlating with expression of ERK1/2MAPKs. FasL expression was similar across all groups. Thymomas may be distinguished from thymic hyperplasia by expression of CD5 and ERK1/2MAPKs. Thymectomy is the preferred treatment for MG patients with thymomas but may not be necessary in MG patients with thymic hyperplasia who are treated with immunosuppressive therapy.
重症肌无力(MG)患者和胸腺瘤患者通常会接受胸腺切除术。然而,对于合并胸腺增生的MG患者是否应进行胸腺切除术仍存在争议。我们旨在研究接受胸腺切除术治疗的合并MG和胸腺增生或胸腺瘤患者的胸腺病理结果,以及免疫抑制的效果。选择33例MG患者并进行如下分组:无胸腺异常患者、胸腺增生患者和胸腺瘤患者。所有患者均接受甲泼尼龙联合免疫抑制治疗。另外选择24例接受胸腺切除术治疗的合并胸腺增生或胸腺瘤的MG患者。作为对照,选择5例无MG的胸腺瘤或胸腺癌患者。检测胸腺中CD5、细胞外调节蛋白激酶1/2丝裂原活化蛋白激酶(ERK1/2MAPKs)和CD95配体(FasL)的表达。与仅患有胸腺瘤的MG患者相比,甲泼尼龙和免疫抑制治疗对胸腺组织正常的MG患者和胸腺增生的MG患者非常有效。CD5表达在胸腺增生的MG患者中最高,与ERK1/2MAPKs的表达相关。FasL表达在所有组中相似。胸腺瘤可通过CD5和ERK1/2MAPKs的表达与胸腺增生相鉴别。胸腺切除术是患有胸腺瘤的MG患者的首选治疗方法,但对于接受免疫抑制治疗的胸腺增生的MG患者可能没有必要。