Tanno Luciana Kase, Chalmers Robert J G, Calderon Moises A, Aymé Ségolène, Demoly Pascal
Hospital Sírio Libanês, São Paulo, Brazil.
Division of Allergy, Department of Pulmonology, Hôpital Arnaud de Villeneuve, University Hospital of Montpellier, 371, av. du Doyen Gaston Giraud, 34295, Montpellier cedex 5, France.
Orphanet J Rare Dis. 2017 Mar 16;12(1):53. doi: 10.1186/s13023-017-0607-3.
Although currently misclassified in the International Classification of Diseases (ICD) and still not officially listed as a rare disease, anaphylaxis is a well-known clinical emergency. Anaphylaxis is now one of the principal headings in the "Allergic and hypersensitivity conditions" section recently compiled for the forthcoming 11 Revision of ICD (ICD-11). We here report the building process used for the pioneering "Anaphylaxis" subsection of ICD-11 in which we aimed for transparency as recommended in the ICD-11 revision guidelines.
During an online intensive scientific and technical discussions with ICD-11 Topic Advisory Groups and Expert Working Groups, we drafted a total of 35 proposals for the classification of anaphylaxis. From all the 35 proposals, 77% were implemented, 20% remain to be implemented, and the others being partially implemented (1.5%) or rejected (1.5%).
For the first time, anaphylaxis is now properly classified and has attained greater visibility within ICD. In addition to all the benefits expected from the actions we have undertaken in updating the terminology, definitions and classification of allergic and hypersensitivity conditions for ICD-11, we strongly believe that anaphylaxis should be a public health priority and that it should therefore be formally added into the list of rare diseases in order to support awareness and quality clinical management of patients.
尽管目前在《国际疾病分类》（ICD）中分类有误且仍未被正式列为罕见病，但过敏反应是一种广为人知的临床急症。过敏反应现已成为为即将到来的ICD第11次修订版（ICD - 11）近期编纂的“过敏和超敏反应性疾病”章节中的主要标题之一。我们在此报告用于ICD - 11开创性“过敏反应”子章节的构建过程，在此过程中我们按照ICD - 11修订指南的建议力求做到透明。
在与ICD - 11主题咨询小组和专家工作组进行的在线密集科学技术讨论期间，我们总共起草了35项关于过敏反应分类的提案。在所有35项提案中，77%得到实施，20%有待实施，其他的部分得到实施（1.5%）或被否决（1.5%）。
过敏反应首次得到了恰当分类，并在ICD中获得了更高的关注度。除了我们为更新ICD - 11中过敏和超敏反应性疾病的术语、定义及分类所采取行动预期带来的所有益处外，我们坚信过敏反应应成为公共卫生重点，因此应正式列入罕见病名单，以提高对患者的认知度并实现优质临床管理。
