Ladouceur Magalie, Pontnau Florence, Iserin Laurence
Hôpital européen Georges-Pompidou, unité des cardiopathies congénitales de l'adultes, cardiologie, centre de référence des malformations cardiaques congénitales complexes, M3C, 20, rue Leblanc, 75015 Paris France.
Hôpital européen Georges-Pompidou, unité des cardiopathies congénitales de l'adultes, cardiologie, centre de référence des malformations cardiaques congénitales complexes, M3C, 20, rue Leblanc, 75015 Paris France.
Presse Med. 2017 May;46(5):523-529. doi: 10.1016/j.lpm.2017.02.003. Epub 2017 Mar 14.
The population of adults with congenital heart disease (ACHD) is continuously increasing with now a higher prevalence than that of the pediatric population. This concerns above all complex congenital heart diseases. Heart failure is the primary cause of death followed by arrhythmia, which is very common in ACHD. A specialized follow-up by dedicated centers is significantly associated with an improvement of survival of ACHD patients compared to non-expert follow-up. Extracardiac disorders (liver, kidney, respiratory) are frequent and require an accurate and specific management. The psychosocial impact, particularly the professional difficulties, is common and may require implementation of appropriate measures to improve the patient social life. Unplanned pregnancy and/or a lack of information about contraception may induce severe cardiovascular complications in ACHD women. Education about contraceptive methods at adolescence and pre-conceptional counseling are requested in this population.
患有先天性心脏病（ACHD）的成年人口数量持续增加，目前其患病率高于儿科人群。这尤其涉及复杂的先天性心脏病。心力衰竭是主要死因，其次是心律失常，心律失常在ACHD中非常常见。与非专业随访相比，由专门中心进行的专业随访与ACHD患者生存率的提高显著相关。心外疾病（肝脏、肾脏、呼吸）很常见，需要准确和具体的管理。心理社会影响，尤其是职业困难，很常见，可能需要采取适当措施来改善患者的社交生活。意外怀孕和/或缺乏避孕信息可能会在ACHD女性中引发严重的心血管并发症。该人群需要在青春期进行避孕方法教育和孕前咨询。
