Go Ramon, Wang David, Ludwin Danielle
Department of Anesthesiology, New York-Presbyterian, Columbia University Medical Center, New York, NY, USA.
Case Rep Anesthesiol. 2017;2017:6408956. doi: 10.1155/2017/6408956. Epub 2017 Feb 20.
Myotonic Dystrophy (DM) affects multiple organ systems. Disorders such as hyperthyroidism, progressive musculoskeletal weakness, cardiac dysrhythmias, hypoventilation, and cognitive-behavioral disorders may be present in these patients. Thorough preoperative assessment and anesthetic planning are required to minimize the risk of anesthetic complications. Patients with DM can exhibit exquisite sensitivity to sedatives, neuromuscular blocking agents, and volatile anesthetics, resulting in potential postoperative complications. There is limited literature available on successful anesthetic techniques for the DM patient. We present this case report to add to our current fund of knowledge.
强直性肌营养不良(DM)会影响多个器官系统。这些患者可能会出现甲状腺功能亢进、进行性肌肉骨骼无力、心律失常、通气不足以及认知行为障碍等病症。需要进行全面的术前评估和麻醉计划,以将麻醉并发症的风险降至最低。DM患者可能对镇静剂、神经肌肉阻滞剂和挥发性麻醉剂表现出极高的敏感性,从而导致潜在的术后并发症。关于DM患者成功麻醉技术的文献有限。我们呈现此病例报告以增加我们目前的知识储备。