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双侧乳房切除及放疗治疗乳腺癌后发生的斯图尔特-特里夫斯综合征:病例报告

Stewart-Treves Syndrome after Bilateral Mastectomy and Radiotherapy for Breast Carcinoma: Case Report.

作者信息

Taşdemir Arzu, Karaman Hatice, Ünal Dilek, Mutlu Hasan

机构信息

Department of Pathology, Kayseri Training and Research Hospital, Kayseri, Turkey.

Department of Oncology, Kayseri Training and Research Hospital, Kayseri, Turkey.

出版信息

J Breast Health. 2015 Apr 1;11(2):92-94. doi: 10.5152/tjbh.2015.1604. eCollection 2015 Apr.

Abstract

Stewart-Treves syndrome is an angiosarcoma that occurs because of chronic lymphedema, which in most cases is a complication after mastectomy with axillary node dissection and postoperative radiation. Prognosis for this rare tumor is poor. The best therapy is early and radical excision. Chronic lymphedema seems to be an important pathogenic factor. We report a 59-year-old patient with chronic lymphedema and lymphangiosarcoma of the left upper limb who had a left modified radical mastectomy with axillary node dissection and postoperative radiation nine years ago. Additionally, the patient underwent a right modified radical mastectomy with axillary node dissection and postoperative radiation one year ago. In this report, we present a case of Stewart-Treves syndrome after the patient was operated for bilateral breast carcinoma, a review of literature, and principles of treatment.

摘要

斯图尔特-特里夫斯综合征是一种因慢性淋巴水肿而发生的血管肉瘤,在大多数情况下,慢性淋巴水肿是乳房切除加腋窝淋巴结清扫及术后放疗后的并发症。这种罕见肿瘤的预后很差。最佳治疗方法是早期根治性切除。慢性淋巴水肿似乎是一个重要的致病因素。我们报告一例59岁患有左上肢慢性淋巴水肿和淋巴管肉瘤的患者,该患者9年前接受了左改良根治性乳房切除术加腋窝淋巴结清扫及术后放疗。此外,患者1年前接受了右改良根治性乳房切除术加腋窝淋巴结清扫及术后放疗。在本报告中,我们介绍了一例双侧乳腺癌手术后发生斯图尔特-特里夫斯综合征的病例、文献综述及治疗原则。

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