Pinho Elika, Gomes Andre Amaral, Silva Maria Joao, Torres Tiago Pinheiro, Coelho Andreia, Almeida Pedro Bernardo, Lourenco Patricia, Bettencourt Paulo
Servico de Medicina Interna, Centro Hospitalar Sao Joao, Portugal.
Servico de Cardiologia, Centro Hospitalar Sao Joao, Portugal.
Cardiol Res. 2013 Feb;4(1):41-44. doi: 10.4021/cr254e. Epub 2013 Mar 8.
Atrial Septal Defect (ASD) is one of the most frequently congenital heart diseases in adults and it is often asymptomatic until adulthood. We report a case of a 90-year-old woman admitted to hospital with dyspnea and orthopnea insidiously progressing over the preceding 5 years and becoming severe with dyspnea on minimal activities, orthopnea and paroxysmal nocturnal dyspnea, in the last 2 weeks. The transthoracic echocardiogram revealed an atrial septal defect ostium secundum type, with left-to-right shunt, moderate to severe tricuspid insufficiency, severe pulmonary hypertension (72 mmHg) and preserved biventricular function. With diuretic therapy optimization the patient showed symptomatic improvement. This present case represents and unusual and very late presentation of an atrial septal defect ostium secundum type, which is usually diagnosed at the mild adult age. Our patient lived symptom-free for over 80 years.
房间隔缺损(ASD)是成人中最常见的先天性心脏病之一,通常在成年前无症状。我们报告一例90岁女性患者,因呼吸困难和端坐呼吸入院,在过去5年中症状隐匿进展,在过去2周内,轻微活动即出现呼吸困难、端坐呼吸和阵发性夜间呼吸困难且症状加重。经胸超声心动图显示继发孔型房间隔缺损,伴有左向右分流、中度至重度三尖瓣反流、重度肺动脉高压(72 mmHg),双心室功能保留。通过优化利尿治疗,患者症状有所改善。本病例代表了继发孔型房间隔缺损一种不寻常且非常晚期的表现,该疾病通常在成年早期被诊断。我们的患者在80多年里一直无症状。