Choksi Vivek, Dave Kairavee, Cantave Rulz, Shaharyar Sameer, Joseph Jeevan, Shankar Uday, Kaplan Steven, Feiz Hamid
Aventura Hospital & Medical Center, Aventura, FL, USA.
Case Rep Gastrointest Med. 2017;2017:4815752. doi: 10.1155/2017/4815752. Epub 2017 Mar 5.
Acute esophageal necrosis (AEN) also known as "black esophagus" or necrotizing esophagitis is a rare syndrome characterized by a striking diffuse patchy or circumferential black appearance of the esophageal mucosa that preferentially affects the distal esophagus and terminates at the gastroesophageal junction. Only 88 patients over a span of 40 years have received this diagnosis, and the prevalence of this disease ranges from 0.001 to 0.2% of cases in literature. It more commonly affects men (4 : 1 ratio) in the sixth decade of life. It is associated with a high mortality rate, approaching 32%. We report a case of AEN presenting in the setting of diabetic ketoacidosis (DKA), affecting both the proximal and distal esophagus.
急性食管坏死(AEN),也被称为“黑色食管”或坏死性食管炎,是一种罕见的综合征,其特征是食管黏膜呈现出显著的弥漫性斑片状或环形黑色外观,主要累及食管远端,并在胃食管交界处终止。在40年的时间里,仅有88例患者被诊断为此病,文献报道该疾病的患病率在0.001%至0.2%之间。它在60岁左右的男性中更为常见(男女比例为4∶1)。其死亡率较高,接近32%。我们报告一例在糖尿病酮症酸中毒(DKA)背景下出现的急性食管坏死病例,该病例累及食管近端和远端。