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伴有舞蹈症的神经白塞病

Neuro-Behçet's Disease with Chorea.

作者信息

Gür Özmen Selen, Hanağasi Haşmet, Gürvit Hakan, Emre Murat, Akman Demir Gülşen

机构信息

Department of Neuroscience, Institute for Experimental and Medical Research (DETAE), Istanbul University, İstanbul, Turkey; Clinic of Neurology, Iğdır State Hospital, Iğdır, Turkey.

Department of Neurology, İstanbul University İstanbul Faculty of Medicine, İstanbul, Turkey.

出版信息

Noro Psikiyatr Ars. 2015 Jun;52(2):200-201. doi: 10.5152/npa.2015.7316. Epub 2015 Jun 1.

DOI:10.5152/npa.2015.7316
PMID:28360705
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5353199/
Abstract

Behçet's disease (BD) was described as a three-symptom complex comprising uveitis, oral aphthae, and genital ulcerations. It is a multisystemic, recurrent, inflammatory disorder and it is of unknown cause. Neuro-Behçet (NB) is present in 5%-7% of BD. Movement disorders have rarely been reported in NB. Here, we report a case of chronic parenchymal NB presenting with chorea.

摘要

白塞病(BD)被描述为一种由葡萄膜炎、口腔溃疡和生殖器溃疡组成的三联征。它是一种多系统、复发性炎症性疾病,病因不明。神经白塞病(NB)在5%-7%的白塞病患者中出现。NB患者很少有运动障碍的报道。在此,我们报告一例以舞蹈症为表现的慢性实质性NB病例。

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本文引用的文献

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Neuro-Behçet's disease in Caucasians: a study of 22 patients.高加索人群中的神经白塞病:22例患者的研究
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Rinsho Shinkeigaku. 2001 Jan;41(1):45-9.
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Chorea and jaw-opening dystonia as a manifestation of NeuroBehcet's syndrome.舞蹈症和张口肌张力障碍作为神经白塞病综合征的一种表现
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