Gür Özmen Selen, Hanağasi Haşmet, Gürvit Hakan, Emre Murat, Akman Demir Gülşen
Department of Neuroscience, Institute for Experimental and Medical Research (DETAE), Istanbul University, İstanbul, Turkey; Clinic of Neurology, Iğdır State Hospital, Iğdır, Turkey.
Department of Neurology, İstanbul University İstanbul Faculty of Medicine, İstanbul, Turkey.
Noro Psikiyatr Ars. 2015 Jun;52(2):200-201. doi: 10.5152/npa.2015.7316. Epub 2015 Jun 1.
Behçet's disease (BD) was described as a three-symptom complex comprising uveitis, oral aphthae, and genital ulcerations. It is a multisystemic, recurrent, inflammatory disorder and it is of unknown cause. Neuro-Behçet (NB) is present in 5%-7% of BD. Movement disorders have rarely been reported in NB. Here, we report a case of chronic parenchymal NB presenting with chorea.
白塞病(BD)被描述为一种由葡萄膜炎、口腔溃疡和生殖器溃疡组成的三联征。它是一种多系统、复发性炎症性疾病,病因不明。神经白塞病(NB)在5%-7%的白塞病患者中出现。NB患者很少有运动障碍的报道。在此,我们报告一例以舞蹈症为表现的慢性实质性NB病例。