West Emily S, Shinkai Kanade, Ai Weiyun Z, Pincus Laura B
Department of Dermatology, University of California at San Francisco, San Francisco, California.
Department of Medicine, Division of Hematology/Oncology, University of California at San Francisco, San Francisco, California.
JAAD Case Rep. 2017 Mar 20;3(2):87-89. doi: 10.1016/j.jdcr.2016.12.007. eCollection 2017 Mar.
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare form of cutaneous T-cell lymphoma characterized by neoplastic α/β T cells infiltrating subcutaneous tissues in a lobular pattern. Few data support the optimal treatment regimen for patients, given the rarity of this condition, and even fewer data describe treatment when diagnosed during pregnancy. We describe a case of SPTCL in a pregnant patient who achieved clinical remission after treatment with corticosteroid monotherapy. Our case suggests that corticosteroids should be considered as first-line treatment in pregnant patients with SPTCL.
皮下脂膜炎样T细胞淋巴瘤(SPTCL)是一种罕见的皮肤T细胞淋巴瘤,其特征为肿瘤性α/β T细胞呈小叶状浸润皮下组织。鉴于这种疾病的罕见性,几乎没有数据支持针对患者的最佳治疗方案,而且关于妊娠期间诊断出该病时的治疗数据更少。我们描述了一例妊娠患者的SPTCL病例,该患者接受皮质类固醇单药治疗后实现了临床缓解。我们的病例表明,皮质类固醇应被视为妊娠SPTCL患者的一线治疗药物。