Quinn Emily D, Rowland Charity
Vanderbilt University, Nashville, TN.
Oregon Health & Science University, Portland, OR.
Am J Speech Lang Pathol. 2017 May 17;26(2):369-382. doi: 10.1044/2016_AJSLP-15-0075.
This study explores data on expressive communication skills of 300 individuals aged 0.0-21.11 years with Angelman syndrome (AS). These data provide a composite portrait of communication skills in a large sample of children and young adults with this rare disorder, specifying new detailed information about expressive communication.
The database associated with the Communication Matrix assessment (Rowland, 2004, 2011; Rowland & Fried-Oken, 2010) was mined for data regarding individuals with AS. We extracted data on the reasons for communicating, level of communication achieved, and use of various expressive communication modes to convey 24 specific messages. The performance of children and young adults in 5 age groups in the cross-sectional sample were contrasted.
Results confirmed earlier studies showing that few individuals with AS use natural speech. However, in addition to using presymbolic modes, many children used alternative symbolic modes such as picture symbols, object symbols, and manual signs. Assessment scores increased slightly with age, F(4, 295) = 2.416, p = .049.
Aggregating data on a large sample of individuals with AS provides a reference point for practitioners and family members and a basis for future investigations.
本研究探讨了300名年龄在0.0至21.11岁之间的天使综合征（AS）患者的表达性沟通技巧数据。这些数据提供了患有这种罕见疾病的大量儿童和年轻人沟通技巧的综合概况，明确了有关表达性沟通的新的详细信息。
挖掘与沟通矩阵评估相关的数据库（罗兰，2004年、2011年；罗兰和弗里德-奥肯，2010年），以获取有关AS患者的数据。我们提取了关于沟通原因、所达到的沟通水平以及使用各种表达性沟通模式来传达24条特定信息的数据。对横断面样本中5个年龄组的儿童和年轻人的表现进行了对比。
结果证实了早期研究的结果，即很少有AS患者使用自然语言。然而，除了使用前符号模式外，许多儿童还使用了替代符号模式，如图像符号、物体符号和手势。评估分数随年龄略有增加，F(4, 295) = 2.416，p = .049。
汇总大量AS患者的数据为从业者和家庭成员提供了一个参考点，并为未来的研究奠定了基础。
