Deng Xiaofeng, Zhang Dong, Zhang Yan, Wang Rong, Wang Bo, Zhao Jizong
Department of Neurosurgery, Beijing Tiantan Hospital, Capital Medical University, China National Clinical Research Center for Neurological Diseases (NCRC-ND), Center of Stroke, Beijing Institute for Brain Disorders, Beijing Key Laboratory of Translational Medicine for Cerebrovascular Disease, Beijing, China.
State Key Laboratory of Brain and Cognitive Science, Beijing MRI Center for Brain Research, Institute of Biophysics, Chinese Academy of Sciences, Beijing, China.
J Clin Neurosci. 2017 Aug;42:116-118. doi: 10.1016/j.jocn.2017.03.043. Epub 2017 Apr 4.
The main change of moyamoya disease (MMD) is steno-occlusion at the terminal portion of the bilateral internal carotid arteries (ICAs). Occlusion of distal portions of the bilateral vertebral arteries (VAs) in MMD has never been reported. An 18-year old female was admitted with repeated headache for 13years. Cerebral digital subtraction angiography (DSA) demonstrated occlusion of bilateral ICAs at their terminal portions, moyamoya vessels at the skull base, occlusion of bilateral distal VAs and the basilar artery (BA) fed by the tortuous collateral vessels arising from the cervical segment of VAs. We report this unique case for its rarity and discuss its mechanism.
烟雾病(MMD)的主要变化是双侧颈内动脉(ICA)末端的狭窄闭塞。烟雾病中双侧椎动脉(VA)远端闭塞的情况从未有过报道。一名18岁女性因反复头痛13年入院。脑数字减影血管造影(DSA)显示双侧ICA末端闭塞、颅底烟雾状血管、双侧VA远端闭塞以及由VA颈段迂曲侧支血管供血的基底动脉(BA)。我们报告这一罕见的独特病例并讨论其机制。