Rosemberg Dov Lagus, Akkari Miguel, Braga Susana Dos Reis, Lenza Mario, Martins Fabio Ricardo Picchi, Santili Claudio
Faculdade de Ciências Médicas da Santa Casa de Misericórdia de São Paulo, São Paulo, SP, Brazil.
Hospital Israelita Albert Einstein, São Paulo, SP, Brazil.
Rev Bras Ortop. 2017 Mar 11;52(2):228-232. doi: 10.1016/j.rboe.2017.03.006. eCollection 2017 Mar-Apr.
Type B hemophilia usually affects patients with a family history of this disease and has a typical clinical picture. However, in the present case it appeared in a patient outside the typical age with no family history of hematologic malignancies and with an unusual clinical picture.
B型血友病通常影响有该疾病家族史的患者,且具有典型的临床表现。然而,在本病例中,它出现在一名非典型年龄的患者身上,该患者没有血液系统恶性肿瘤家族史,且临床表现异常。