Zhu Xuefei, Ma Xiaolu, Tu Yingfeng, Huang Min, Liu Hongmei, Wang Fengli, Gong Juanjuan, Wang Jiuqiang, Li Xiaoling, Chen Qian, Shen Hongyan, Zhu Shu, Wang Yun, Liu Yang, Guo Caixia, Tang Tie-Shan
State Key Laboratory of Membrane Biology, Institute of Zoology, University of Chinese Academy of Sciences, Chinese Academy of Sciences, Beijing 100101, China.
CAS Key Laboratory of Genomics and Precision Medicine, Beijing Institute of Genomics, University of Chinese Academy of Sciences, Chinese Academy of Sciences, Beijing 100101, China.
Oncotarget. 2017 May 30;8(22):36423-36437. doi: 10.18632/oncotarget.16855.
Deficiency of Parkin is a major cause of early-onset Parkinson's disease (PD). Notably, PD patients also exhibit a significantly higher risk in melanoma and other skin tumors, while the mechanism remains largely unknown. In this study, we show that depletion of Parkin causes compromised cell viability and genome stability after ultraviolet (UV) radiation. We demonstrate that Parkin promotes efficient Rad18-dependent proliferating cell nuclear antigen (PCNA) monoubiquitination by facilitating the formation of Replication protein A (RPA)-coated ssDNA upon UV radiation. Furthermore, Parkin is found to physically interact with NBS1 (Nijmegen breakage syndrome 1), and to be required for optimal recruitment of NBS1 and DNA polymerase eta (Polη) to UV-induced damage sites. Consequently, depletion of Parkin leads to increased UV-induced mutagenesis. These findings unveil an important role of Parkin in protecting genome stability through positively regulating translesion DNA synthesis (TLS) upon UV damage, providing a novel mechanistic link between Parkin deficiency and predisposition to skin cancers in PD patients.
帕金蛋白缺乏是早发性帕金森病(PD)的主要病因。值得注意的是,PD患者患黑色素瘤和其他皮肤肿瘤的风险也显著更高,而其机制在很大程度上仍不清楚。在本研究中,我们发现帕金蛋白缺失会导致紫外线(UV)辐射后细胞活力受损和基因组稳定性下降。我们证明,帕金蛋白通过促进紫外线辐射后复制蛋白A(RPA)包被的单链DNA的形成,促进依赖Rad18的增殖细胞核抗原(PCNA)单泛素化。此外,我们发现帕金蛋白与NBS1(尼曼-匹克氏病综合征1)存在物理相互作用,并且是将NBS1和DNA聚合酶η(Polη)最佳招募到紫外线诱导的损伤位点所必需的。因此,帕金蛋白缺失会导致紫外线诱导的诱变增加。这些发现揭示了帕金蛋白在紫外线损伤时通过正向调节跨损伤DNA合成(TLS)来保护基因组稳定性的重要作用,为帕金蛋白缺乏与PD患者患皮肤癌易感性之间提供了一种新的机制联系。