Jonsson Dagur Ingi, Pirskanen Ritva, Piehl Fredrik
Karolinska University Hospital, Department of Neurology, Stockholm, Sweden.
Karolinska University Hospital, Department of Neurology, Stockholm, Sweden; Karolinska Institutet, Department of Clinical Neuroscience, Stockholm, Sweden.
Neuromuscul Disord. 2017 Jun;27(6):565-568. doi: 10.1016/j.nmd.2017.03.007. Epub 2017 Mar 16.
Muscle fatigue associated with myasthenia gravis is caused by autoantibodies interfering with neuromuscular transmission. Immunomodulating treatment is widely used in moderate to severe myasthenia, although the use of newer biological drugs except rituximab is rare. We describe the effect of tocilizumab, a blocker of interleukin-6 signalling, in two female myasthenia patients with high titres of serum acetylcholine receptor antibodies and insufficient response to rituximab. The first patient had been treated with high dose immunoglobulins regularly for several years and the second patient had been treated both with different oral immune suppressants and immunoglobulins before testing a low dose of rituximab without significant clinical effect. Subsequent treatment with tocilizumab resulted in clinical improvement within a few months. The first patient was switched back to rituximab, which resulted in worsening until tocilizumab was restarted. Tocilizumab can be a therapeutic option in cases not responding to rituximab.
重症肌无力相关的肌肉疲劳是由自身抗体干扰神经肌肉传递引起的。免疫调节治疗广泛用于中重度重症肌无力,不过除利妥昔单抗外,新型生物药物的使用较少。我们描述了白细胞介素-6信号阻滞剂托珠单抗对两名血清乙酰胆碱受体抗体滴度高且对利妥昔单抗反应不足的女性重症肌无力患者的疗效。第一名患者多年来定期接受高剂量免疫球蛋白治疗,第二名患者在试用低剂量利妥昔单抗且无明显临床效果之前,曾接受过不同的口服免疫抑制剂和免疫球蛋白治疗。随后使用托珠单抗治疗,数月内临床症状得到改善。第一名患者重新使用利妥昔单抗后病情恶化,直到重新开始使用托珠单抗。对于对利妥昔单抗无反应的病例,托珠单抗可能是一种治疗选择。