Sawazaki Harutake, Araki Daiji, Miyata Kazunori, Ito Keiichi
Department of Urology, Tama-hokubu Medical Center, Higashimurayama, Japan.
Department of Urology, National Defense Medical College, Tokorozawa, Japan.
Urol Case Rep. 2017 Apr 19;13:45-47. doi: 10.1016/j.eucr.2016.10.014. eCollection 2017 Jul.
Renal replacement lipomatosis (RRL) is a rare condition that occurs at the end of the spectrum of renal tissue replacement by fat. Xanthogranulomatous pyelonephritis (XGP) is a granulomatous inflammation characterized by destruction of renal parenchyma and replacement by lipid-laden macrophages. We present the case of a 75-year-old man who complained of severe anemia 34 years after right nephrolithotomy. Computed tomography revealed a huge low-density mass with renal parenchyma atrophy on the right side of horseshoe kidney. Right nephrectomy was performed. Pathological diagnosis was RRL with XGP. This is the first report of RRL with XGP in a horseshoe kidney.
肾替代脂肪瘤病（RRL）是一种罕见的疾病，发生于肾组织被脂肪替代的谱系末端。黄色肉芽肿性肾盂肾炎（XGP）是一种肉芽肿性炎症，其特征为肾实质破坏并被充满脂质的巨噬细胞替代。我们报告一例75岁男性病例，该患者在右肾切开取石术后34年出现严重贫血。计算机断层扫描显示马蹄肾右侧有一个巨大的低密度肿块，伴有肾实质萎缩。进行了右肾切除术。病理诊断为合并XGP的RRL。这是马蹄肾中合并XGP的RRL的首例报告。
