Tan Grace Hwei Ching, Ng Deanna, Hennedige Tiffany, Teo Melissa
Division of Surgical Oncology, National Cancer Centre Singapore, Singapore, Singapore.
BMJ Case Rep. 2017 May 5;2017:bcr-2016-218202. doi: 10.1136/bcr-2016-218202.
We present a case of a solitary fibrous tumour (SFT) resembling an aggressive angiomyxoma/liposarcoma on radiological imaging, causing significant diagnostic challenges preoperatively. A 76-year-old male was incidentally found to have a large pelvic mass on a CT scan. Further evaluation with an MRI scan confirmed a presacral mass containing fat and soft tissue components. It was inseparable from the sacrococcygeal spine, rectal serosa and the posterior wall of the urinary bladder, but no evidence of invasion was seen. A prominent vascular pedicle arising from the epidural vasculature was also noted. Differentials discussed at the multidisciplinary tumour board were an aggressive angiomyxoma versus a liposarcoma. The patient underwent wide resection of the pelvic tumour, anterior resection and end colostomy. Intraoperatively, a large 20 cm pelvic mass involving the sigmoid mesocolon and presacral fascia was found. Final histology reported an SFT with extensive adipocytic metaplasia.
我们报告一例在放射影像学上类似侵袭性血管黏液瘤/脂肪肉瘤的孤立性纤维瘤(SFT),术前造成了重大的诊断挑战。一名76岁男性在CT扫描时偶然发现盆腔有一个大肿块。通过MRI扫描进一步评估证实骶前有一个包含脂肪和软组织成分的肿块。它与骶尾椎、直肠浆膜和膀胱后壁无法分离,但未见侵袭迹象。还注意到有一个由硬膜外血管系统发出的明显血管蒂。多学科肿瘤讨论会上讨论的鉴别诊断包括侵袭性血管黏液瘤与脂肪肉瘤。患者接受了盆腔肿瘤广泛切除术、前切除术和结肠造口术。术中发现一个20厘米的大盆腔肿块,累及乙状结肠系膜和骶前筋膜。最终组织学报告为伴有广泛脂肪化生的SFT。