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先天性巨大右心房瘤:超声心动图诊断与外科治疗

Congenital Giant Right Atrial Aneurysm: Echocardiographic Diagnosis and Surgical Management.

作者信息

Wang Yao, Liu Aijun, Ye Weihua

机构信息

Department of Cardiovascular Surgery, Chinese PLA General Hospital, Beijing,China.

出版信息

Heart Surg Forum. 2017 Apr 28;20(2):E055-E057. doi: 10.1532/hsf.1656.

Abstract

Congenital right atrial aneurysm is a rare abnormality and may easily be confused with various anomalies, such as pericardial effusion, pericardial cysts, tumors, and Ebstein's anomaly. Patients with right atrial aneurysm may be asymptomatic; but some patients may develop life-threatening complications, such as arrhythmias, congestive heart failure, or pulmonary embolism. Therefore, it is essential for correct diagnosis and appropriate patient management. We report a case of giant right atrial aneurysm in a 7-year-old boy who presented with progressive protrusion of chest. Echocardiography established the definitive diagnosis and surgical resection was successful.

摘要

先天性右心房动脉瘤是一种罕见的异常情况,很容易与各种异常情况相混淆,如心包积液、心包囊肿、肿瘤和埃布斯坦畸形。右心房动脉瘤患者可能没有症状;但有些患者可能会出现危及生命的并发症,如心律失常、充血性心力衰竭或肺栓塞。因此,正确诊断和适当的患者管理至关重要。我们报告一例7岁男孩的巨大右心房动脉瘤病例,该男孩表现为胸部逐渐隆起。超声心动图明确了诊断,手术切除成功。

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