Singh Satyendra Narayan, Bhatt Trilok C
Surg Cdr and Associate Professor, Department of Radiology, Base Hospital, Delhi Cantt, New Delhi, India.
Surg Lt Cdr, Department of Radiology, INHS Kalyani, Visakhapatnam, Andhra Pradesh, India.
J Clin Diagn Res. 2017 Mar;11(3):TD06-TD08. doi: 10.7860/JCDR/2017/24123.9554. Epub 2017 Mar 1.
Complete absence of Inferior Vena Cava (IVC) is a rare anomaly with a reported incidence of 0.0005% to 1%. This is often asymptomatic with incidental detection during cross-sectional imaging. It may also present with deep venous thrombosis, pulmonary thromboembolism or compressive symptoms in form of nerve root compression. Pelvic Congestion Syndrome (PCS) is an increasingly recognized entity with well laid out diagnostic criteria and evolving management protocols. Complete absence of IVC is a rare cause of pelvic congestion syndrome. We present a case of young female presenting with symptoms typical of pelvic venous congestion who was found to have complete absence of IVC as the underlying cause. She also had associated small left kidney with compensatory hypertrophy of the right kidney which is another rare association.
下腔静脉完全缺如是一种罕见的异常情况，报告的发生率为0.0005%至1%。这种情况通常无症状，多在横断面成像检查时偶然发现。它也可能表现为深静脉血栓形成、肺血栓栓塞或神经根受压形式的压迫症状。盆腔充血综合征（PCS）是一个越来越被认可的病症，有明确的诊断标准和不断发展的治疗方案。下腔静脉完全缺如是盆腔充血综合征的罕见病因。我们报告一例年轻女性，表现出典型的盆腔静脉充血症状，经检查发现病因是下腔静脉完全缺失。她还伴有左肾较小，右肾代偿性肥大，这也是一种罕见的关联情况。
