系统性红斑狼疮的不典型表现。
Unusual presentation of systemic lupus erythematosus.
作者信息
Mahesh E, Madhyastha Parampalli Rakesh, Varma Vijay, Gurudev K C, Gireesh M S, Bande Sujeeth Reddy
机构信息
Department of Nephrology, M. S. Ramaiah Memorial Hospital, Bengaluru, Karnataka, India.
出版信息
Saudi J Kidney Dis Transpl. 2017 May-Jun;28(3):653-656. doi: 10.4103/1319-2442.206468.
Bullous systemic lupus erythematosus is a rare distinctive subepidermal blistering disorder that can occur in patients with systemic lupus erythematosus (SLE). It is histologically characterized by a neutrophil-predominant infiltrate in the subepidermal region with deposition of immunoglobulins (IgG, IgA, IgM), C3, and auto-antibodies against collagen VII. Herein, we report a case of a 13-year-old girl who presented with bullous SLE and Class III lupus nephritis, which is extremely rare at this age.
大疱性系统性红斑狼疮是一种罕见的、独特的表皮下大疱性疾病，可发生于系统性红斑狼疮（SLE）患者。其组织学特征为表皮下区域以中性粒细胞为主的浸润，伴有免疫球蛋白（IgG、IgA、IgM）、C3以及抗VII型胶原自身抗体的沉积。在此，我们报告一例13岁女孩，她患有大疱性SLE和III级狼疮性肾炎，这种情况在这个年龄段极为罕见。
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