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胎盘间充质发育异常:伴有大体及组织学表现的病例报告

Placental mesenchymal dysplasia: case report with gross and histological findings.

作者信息

Toscano Marcello Pecoraro, Schultz Regina

机构信息

Anatomic Pathology Division - Hospital das Clínicas - Faculdade de Medicina - Universidade de São Paulo, São Paulo/SP, Brazil.

出版信息

Autops Case Rep. 2014 Mar 30;4(4):51-56. doi: 10.4322/acr.2014.039. eCollection 2014 Oct-Dec.

Abstract

Placental mesenchymal dysplasia (PMD) is a rare placental disorder characterized by placental enlargement and areas of abnormal, enlarged, grape-like villi. This condition may resemble a partial hydatidiform mole and may occur associated with Beckwith-Wiedemann syndrome (BWS) or in phenotypically normal fetuses. There were 110 cases reported so far. We describe one case with typical gross and microscopic placental lesions.

摘要

胎盘间充质发育异常(PMD)是一种罕见的胎盘疾病,其特征为胎盘增大以及存在异常、增大的葡萄样绒毛区域。这种情况可能类似于部分性葡萄胎,可能与贝克威思-维德曼综合征(BWS)相关,或发生于表型正常的胎儿。迄今为止共报道了110例病例。我们描述了1例具有典型大体及镜下胎盘病变的病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0142/5443133/53ee9814b621/autopsy-04-04051-g01.jpg

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