Toscano Marcello Pecoraro, Schultz Regina
Anatomic Pathology Division - Hospital das Clínicas - Faculdade de Medicina - Universidade de São Paulo, São Paulo/SP, Brazil.
Autops Case Rep. 2014 Mar 30;4(4):51-56. doi: 10.4322/acr.2014.039. eCollection 2014 Oct-Dec.
Placental mesenchymal dysplasia (PMD) is a rare placental disorder characterized by placental enlargement and areas of abnormal, enlarged, grape-like villi. This condition may resemble a partial hydatidiform mole and may occur associated with Beckwith-Wiedemann syndrome (BWS) or in phenotypically normal fetuses. There were 110 cases reported so far. We describe one case with typical gross and microscopic placental lesions.
胎盘间充质发育异常(PMD)是一种罕见的胎盘疾病,其特征为胎盘增大以及存在异常、增大的葡萄样绒毛区域。这种情况可能类似于部分性葡萄胎,可能与贝克威思-维德曼综合征(BWS)相关,或发生于表型正常的胎儿。迄今为止共报道了110例病例。我们描述了1例具有典型大体及镜下胎盘病变的病例。