右位主动脉弓伴正常位心常预示着血管环的存在。
Right aortic arch with situs solitus frequently heralds a vascular ring.
作者信息
Evans William N, Acherman Ruben J, Ciccolo Michael L, Carrillo Sergio A, Mayman Gary A, Luna Carlos F, Rollins Robert C, Castillo William J, Galindo Alvaro, Rothman Abraham, Alexander John A, Kwan Tina W, Restrepo Humberto
机构信息
Children's Heart Center Nevada, Las Vegas, Nevada.
Division of Pediatric Cardiology, Department of Pediatrics, University of Nevada School of Medicine, Las Vegas, Nevada.
出版信息
Congenit Heart Dis. 2017 Sep;12(5):583-587. doi: 10.1111/chd.12487. Epub 2017 Jun 5.
OBJECTIVE
We hypothesized that a right aortic arch in situs solitus, with or without an associated cardiovascular malformation, is often associated with a vascular ring.
METHODS
From those born in Southern Nevada between March 2012 and March 2017, we identified 50 (3.6 per 10,000 live births) with a right aortic arch and situs solitus. From the 50 patients, 6 did not meet inclusion criteria for further analysis.
RESULTS
Of the 44 remaining, 33 (75%) had a vascular ring. Of the 33 with a vascular ring, 26 (79%) occurred with an isolated right aortic arch, and 7 (21%) had an associated cardiovascular malformation. Of the total 44 patients with a right aortic arch in situs solitus, 34 (79%) were diagnosed prenatally.
CONCLUSIONS
In conclusion, we found a right aortic arch in situs solitus was often associated with a vascular ring. Further, to the best of our knowledge, no previous general population study has demonstrated an equal or higher right aortic arch, prenatal detection rate of 79%.
目的
我们推测，孤立性右位主动脉弓，无论有无相关心血管畸形，常与血管环相关。
方法
在2012年3月至2017年3月间出生于内华达州南部的人群中，我们确定了50例（每10000例活产中有3.6例）孤立性右位主动脉弓患者。在这50例患者中，6例不符合进一步分析的纳入标准。
结果
在其余44例患者中，33例（75%）有血管环。在这33例有血管环的患者中，26例（79%）为孤立性右位主动脉弓，7例（21%）有相关心血管畸形。在44例孤立性右位主动脉弓患者中，34例（79%）在产前被诊断。
结论
总之，我们发现孤立性右位主动脉弓常与血管环相关。此外，据我们所知，此前尚无普通人群研究显示右位主动脉弓产前检出率达到或高于79%。
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