原发性肝外胆管神经内分泌肿瘤伴阻塞性黄疸，伪装成肝门部胆管癌。
Primary extrahepatic bile duct neuroendocrine tumor with obstructive jaundice masquerading as a Klatskin tumor.
作者信息
Hoepfner Lauren, White Jared A
机构信息
University of Alabama School of Medicine, University of Alabama Birmingham, Birmingham, AL 35294, USA.
Liver Transplant and Hepatobiliary Surgery, University of Alabama Birmingham, Birmingham, AL 35294, USA.
出版信息
J Surg Case Rep. 2017 Jun 5;2017(6):rjx104. doi: 10.1093/jscr/rjx104. eCollection 2017 Jun.
Neuroendocrine tumors (NETs) of the extrahepatic bile duct are extremely rare and reported infrequently in the literature. These tumors are difficult to diagnose preoperatively, and the prognosis is variable, often determined by extent of disease, tumor grade and resectability. This case report presents a 45-year-old male with history of biliary obstruction relieved by endobiliary stents with common hepatic duct stricture just above the cystic duct, thought to be a Klatskin's cholangiocarcinoma. Final pathological examination was consistent with primary extrahepatic NET.
肝外胆管神经内分泌肿瘤（NETs）极为罕见，文献报道较少。这些肿瘤术前难以诊断，预后各异，通常取决于疾病范围、肿瘤分级和可切除性。本病例报告介绍了一名45岁男性，有胆道梗阻病史，经胆管内支架缓解，肝总管在胆囊管上方狭窄，曾被认为是肝门部胆管癌。最终病理检查结果与原发性肝外NET一致。
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