Lockhart J L, Reeve H R, Krueger R P, Glenn J F, Henry H H
Urology. 1978 Jul;12(1):51-4. doi: 10.1016/0090-4295(78)90366-7.
Two cases of megalourethra are presented, the ninth and tenth cases to be documented in the literature. Both patients exhibited mesodermal abnormalities which justify categorization among the minor forms of prune belly syndrome. One patient, the youngest to have undergone surgical correction, presented with azotemia, dilated posterior urethra, megacystis, and megaureters. The second patient with incomplete or scaphoid form of megalourethra also exhibited undescended testis, corrected by orchiopexy at the time of urethoplasty. In all instances the goal of treatment is preservation of renal function with subsequent functional and anatomic reconstruction of the urinary tract.
本文报告两例巨尿道病例,这是文献记载的第九和第十例。两名患者均表现出中胚层异常,这证明可将其归类为轻型梅干腹综合征。其中一名患者是接受手术矫正的最年轻患者,表现为氮质血症、后尿道扩张、巨膀胱和巨输尿管。第二例患者为不完全或舟状巨尿道,也表现为隐睾,在尿道成形术时通过睾丸固定术进行了矫正。在所有情况下,治疗的目标都是保留肾功能,随后对尿路进行功能和解剖重建。