Department of Pediatric Surgery, St. John's Medical College & Hospital, Bangalore, Karnataka, 560034, India.
Department of Pathology, St. John's Medical College, Bangalore, Karnataka, India.
Indian J Pediatr. 2017 Aug;84(8):618-623. doi: 10.1007/s12098-017-2371-8. Epub 2017 Jun 10.
Hirschsprung disease is a common cause of neonatal and infantile large gut obstruction. It is characterised by varying extent of contiguous aganglionosis extending from the anorectum proximally. Since its recognition, the diagnosis and management has continuously evolved with advances in histological evaluation and surgical techniques. This article summarizes the current modalities of investigation and optimal surgical management of Hirschsprung disease and concludes with a reference to the Indian scenario.
先天性巨结肠是新生儿和婴儿大肠梗阻的常见原因。其特征是从肛直肠近端向近端延伸的不同程度的连续无神经节细胞。自其被认识以来,随着组织学评估和手术技术的进步,其诊断和治疗也在不断发展。本文总结了先天性巨结肠目前的检查方法和最佳手术治疗方法,并提到了印度的情况。