Albarrak Anas Mohammad, Kojan Suleiman
aCollege of Medicine, Prince Sattam Bin Abdulaziz University, Alkharj, Saudi Arabia.
bKing Abdulaziz Medical City/King Saud bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia.
Case Rep Neurol. 2017 Mar 21;9(1):49-53. doi: 10.1159/000466685. eCollection 2017 Jan-Apr.
Idiopathic intracranial hypertension is a rare condition characterized by increased intracranial pressure without clinical, laboratory, or radiological evidence of intracranial pathology. Early management could prevent irreversible outcomes.
A 17-year-old single Arabian female of Arab origin presented with a 2-day complaint of horizontal diplopia and transient visual obscurations. She denied any history of headache or decreased vision. The patient was diagnosed with polycystic ovary syndrome a year prior to presentation. Examination revealed bilateral moderate papilledema and limited left eye abduction. However, visual acuity and fields were normal. Increased intracranial pressure was confirmed by lumbar puncture opening pressure (550 mm H2O). The cerebrospinal fluid composition and imaging of brain and cerebral venous system were normal. The diagnosis of idiopathic intracranial hypertension was confirmed and the patient was treated with acetazolamide 500 mg twice per day. The symptoms totally resolved within 3 days and the papilledema disappeared after 2 months.
Awareness of such uncommon presentation of idiopathic intracranial hypertension emphasizes the critical importance of detailed ophthalmic examination and shows the good prognosis of early management.
特发性颅内高压是一种罕见疾病，其特征为颅内压升高，而无颅内病变的临床、实验室或影像学证据。早期治疗可预防不可逆的后果。
一名17岁单身阿拉伯裔女性，因双眼复视和短暂视力模糊2天前来就诊。她否认有任何头痛或视力下降病史。该患者在就诊前一年被诊断为多囊卵巢综合征。检查发现双侧中度视乳头水肿，左眼外展受限。然而，视力和视野正常。腰椎穿刺初压（550mmH₂O）证实颅内压升高。脑脊液成分以及脑和脑静脉系统的影像学检查均正常。特发性颅内高压诊断明确，患者接受乙酰唑胺治疗，每日两次，每次500mg。症状在3天内完全缓解，视乳头水肿在2个月后消失。
认识到特发性颅内高压这种不常见的表现形式，凸显了详细眼科检查的至关重要性，并表明早期治疗预后良好。
